Strabismus (Squint) – a guide for parents

 

Strabismus, commonly called squint, is an important condition in childhood.  Unrecognised and untreated it may result in permanently reduced vision in the affected eye (lazy eye or amblyopia).  Rarely squint can become manifest due to an inherited defect or disease process within the eye.  A squinting eye can also develop as a result of a neurological defect. 

 

True misalignment of the eyes is uncommon in childhood affecting less than 4% children.  However squint is significantly more common in children with cerebral palsy and also in children with retinopathy and prematurity.  Strabismus is more common within families, particularly when it is related to long sightedness. 

 

Squint in children under one year of age is even less common, affecting only 1% of infants. However we see many referrals with a diagnosis of possible squint in this age group and these children are generally found to have the condition of ‘pseudo squint’. 

 

Surgery squint is certainly not necessary in the majority of the children we see for squint problems. Children, for example, with divergent squint or those in whom squint is related to long-sightedness can be managed without surgery.  Only about 6% of children referred with a possible diagnosis of squint would eventually require surgery.

 

The most important part of management of squint is in fact occlusion therapy (eye patching) and vision can still be maintained in the squinting eye during the period of occlusion therapy.  However in certain types of squint there is a loss of pre-existing binocular function and in these cases surgery is an important part of the management. 

 

Pseudo Squint

The commonest referral we see is for the condition of ‘pseudo suqint’ which may be noticed in infants up to the age of 9 months.  The eye appears misaligned as a convergent squint caused by a broad bridge of the nose (epicanthus).  This is the type of squint that infants are said to ‘grow out of’, for as the child grows the relative effect of the broad bridge (epicanthic folds) is lost.  It is not a true squint and therefore no treatment is required.  However it is often necessary for this diagnosis to be confirmed by an Ophthalmologist or Orthoptist.

 

Convergent Squint / Esotropia 

Infants generally fix and focus clearly by six weeks of age and the eyes are well aligned. Infants can be born with a convergent squint (infantile esotropia) which is commonly seen as an obvious large angle squint turning into the inner corner.  It is an uncommon condition.  Usually the infant will ‘swap’ vision from one eye to the other (cross fixate).  Because of this alternation the infant generally develops good vision in each eye.  Surgery is the treatment for this condition, generally at between 9 to 18 months of age. It is very important that the child continues to be monitored by an Orthoptist following surgery. 

 

Accommodative Esotropia

Some children develop a convergence squint because they are significantly long sighted (hypermetropic). This commonly occurs around the age of two years and can develop quite suddenly.  Due to the effort of having to focus hard, (to overcome the long sightedness), the eyes tend to cross inwards when looking at objects, particularly when looking at objects ‘close up’. The squint can be straightened by wearing spectacles to correct the long sightedness. When they remove the spectacles the squint immediately recurs.  However as the child grows older the long-sightedness generally lessens and they may become less dependant on the spectacle correction.  In some children the squint is only partially corrected by the glasses, and in these children corrective surgery is also necessary. 

 

Divergent Squint / Exotropia

Divergent squint is very uncommon in babies and young infants and it is very important for these infants to be assessed early, as the squint may be a sign of some other more significant defect. 

 

Divergent squint often develops at about the age of 4-5.  The squint is commonly only intermittent initially.  For much of the time the eyes are straight and tend to drift out when the child is tired or ill.  Commonly children with this type of squint tend to ‘squint’ and tend to screw up their eyes in bright sunlight.  In some children the squint becomes less intermittent and more constant requiring corrective surgery.  In a few children the squint may be controlled by correcting a refractive error of myopia (a short sightedness).

 

Vertical Squints

These are less common than horizontal squint and are generally the result of a congenital nerve weakness.  The child may adopt an abnormal head position (head tilt) to control the vertical muscle imbalance. 

 

Squint Due To Eye Defect

Rarely the eyes may become misaligned, (either convergent or divergent), due to a defect within the eye itself.  For example a unilateral cataract, congenital cataract or retinal scar will result in the eye drifting out, as it does not fix properly.  Very rarely a tumour within the eye may manifest as a squint. 

 

Lazy Eye (Amblyopia)

Lazy eye develops when the normal high quality connection between the eye and the visual cortex in the brain is disrupted.  When an infant develops a squint, rather than experience double vision the image from the misaligned eye can be switched off in the visual cortex.  If not corrected this eventually results in permanently reduced vision.  A similar event occurs if the focussing of each eye is markedly different (anisometropia).  This is particularly common if one eye is particularly long sighted or astigmatic. 

 

Occlusion Therapy (Patching)

Patching of the good eye is the treatment advised for amblyopia, (lazy eye), or to prevent amblyopia developing in a squinting eye.  Essentially it is a technique of ‘forcing the eye to see’ without the rivalry of the good eye.  The visual system is considered to be in a state of ‘plasticity’ up to the age of about 8 years. After this age occlusion therapy is generally not very effective. The earlier the treatment given, the better the visual outcome.  Patching treatment is guided and supervised by an Orthoptist. An Orthoptist is an expert in strabismus working alongside the Ophthalmologist. 

 

Surgery For Squint

Surgery is generally undertaken as a day case procedure with full anaesthetic.  It is usually not necessary to cover over the operated eye or eyes after the surgery.  Corrective surgery may be necessary to both eyes, even if the squint is apparent only in one eye.  Children tolerate the surgery well and the eyes are sore for only a few days after the operation.  Following surgery it is very important that the child continues to be monitored by an Orthoptist, certainly up to the age of 8 years old. 

 

Contributed by Mr P Kinnear, Consultant Ophthalmologist.