Chordoma

 

Definition and Presentation

A benign slow growing tumour of the skeleton arising from remnants of the so-called notocord from which the skeleton is formed. These tumours are most commonly found in the lower spine or sacrum but the second most frequent location is the skull base. Presenting symptoms such as headache, double vision are the most common, followed by swallowing difficulties and facial numbness or pain.

 

Diagnosis

MRI and CT are important for diagnosis but the final differentiation from chondrosarcoma and other tumours is made by microscopic examination of a surgical specimen (biopsy).

 

Treatment

The treatment of choice is surgical resection. These tumours are notorious for recurring even many years following what was believed to be a total resection. Due to the difficult location in the centre of the skull base they are also often difficult to remove radically. They are considered to be more radio-resistant than chondrosarcomas. Gamma Knife surgery should therefore be a very attractive post-operative adjunctive treatment. Positive experiences from this combined therapy have been reported but the numbers of patients treated is still low.

 

chordom pre   chordom post
Pre   20 months post